Peter Ljubenkov, MD

Associate Professor
+1 415 476-6880
Fields of Interest

Peter A. Ljubenkov, MD, is a behavioral neurologist at the UCSF Edward and Pearl Fein Memory and Aging Center, where he specializes in caring for patients experiencing cognitive, language, and behavioral changes due to neurological conditions such as Alzheimer’s disease, Lewy body dementia, and other forms of dementia. He has particular expertise in diagnosing and treating frontotemporal dementia and related conditions, including progressive supranuclear palsy and corticobasal degeneration.

Dr. Ljubenkov serves as the director of the UCSF Alzheimer’s Infusion Core and the associate director of the Alzheimer’s Disease and Frontotemporal Degeneration Clinical Trials Program at Fein Memory and Aging Center. He is deeply involved in clinical trials investigating potential therapies for neurodegenerative diseases. His research focuses on identifying biomarkers for frontotemporal dementia, with an emphasis on understanding the role of immune system dysregulation in disease progression.

Dr. Ljubenkov earned his medical degree from the Lewis Katz School of Medicine at Temple University. He completed an internal medicine internship at the University of California, Irvine, followed by a neurology residency at the University of California, San Diego. He then completed a fellowship in behavioral neurology at UCSF and joined the faculty. Since joining UCSF, Dr. Ljubenkov has been actively engaged in research through the Boxer Lab, which is dedicated to advancing treatments and understanding of frontotemporal lobar degeneration. He also served as the 2017–2018 Advancing Research and Treatment for Frontotemporal Lobar Degeneration (ARTFL) research fellow.

Publications

Author Correction: Large-scale network analysis of the cerebrospinal fluid proteome identifies molecular signatures of frontotemporal lobar degeneration.

Saloner R, Staffaroni AM, Dammer EB, Johnson ECB, Paolillo EW, Wise A, Heuer HW, Forsberg LK, Lario-Lago A, Webb JD, Vogel JW, Santillo AF, Hansson O, Kramer JH, Miller BL, Li J, Loureiro J, Sivasankaran R, Worringer KA, Seyfried NT, Yokoyama JS, Spina S, Grinberg LT, Seeley WW, VandeVrede L, Ljubenkov PA, Bayram E, Bozoki A, Brushaber D, Considine CM, Day GS, Dickerson BC, Domoto-Reilly K, Faber K, Galasko DR, Gendron T, Geschwind DH, Ghoshal N, Graff-Radford N, Hales CM, Honig LS, Hsiung GR, Huey ED, Kornak J, Kremers W, Lapid MI, Lee SE, Litvan I, McMillan CT, Mendez MF, Miyagawa T, Pantelyat A, Pascual B, Masdeu J, Paulson HL, Petrucelli L, Pressman P, Rademakers R, Ramos EM, Rascovsky K, Roberson ED, Savica R, Snyder A, Sullivan AC, Tartaglia MC, Vandebergh M, Boeve BF, Rosen HJ, Rojas JC, Boxer AL, Casaletto KB, ALLFTD Consortium

Large-scale network analysis of the cerebrospinal fluid proteome identifies molecular signatures of frontotemporal lobar degeneration.

Saloner R, Staffaroni AM, Dammer EB, Johnson ECB, Paolillo EW, Wise A, Heuer HW, Forsberg LK, Lario-Lago A, Webb JD, Vogel JW, Santillo AF, Hansson O, Kramer JH, Miller BL, Li J, Loureiro J, Sivasankaran R, Worringer KA, Seyfried NT, Yokoyama JS, Spina S, Grinberg LT, Seeley WW, VandeVrede L, Ljubenkov PA, Bayram E, Bozoki A, Brushaber D, Considine CM, Day GS, Dickerson BC, Domoto-Reilly K, Faber K, Galasko DR, Gendron T, Geschwind DH, Ghoshal N, Graff-Radford N, Hales CM, Honig LS, Hsiung GR, Huey ED, Kornak J, Kremers W, Lapid MI, Lee SE, Litvan I, McMillan CT, Mendez MF, Miyagawa T, Pantelyat A, Pascual B, Masdeu J, Paulson HL, Petrucelli L, Pressman P, Rademakers R, Ramos EM, Rascovsky K, Roberson ED, Savica R, Snyder A, Sullivan AC, Tartaglia MC, Vandebergh M, Boeve BF, Rosen HJ, Rojas JC, Boxer AL, Casaletto KB, ALLFTD Consortium

Clinical performance of plasma P-tau217 for the identification of primary Alzheimer’s disease pathology or co-pathology in sporadic frontotemporal dementia.

Igor Prufer Q C Araujo, Julio C. Rojas, Lawren VandeVrede, Peter A. Ljubenkov, Hilary W. Heuer, Bruce L. Miller, William W. Seeley, Adam M. Staffaroni, Binita Rajbanshi, Argentina Lario Lago, Elisabeth H Thijssen, Gianina Toller, Nicholas Proctor, Leah K. Forsberg, Leah K. Forsberg, Danielle Brushaber, Eliana Marisa Ramos, Giovanni Coppola, Brian Appleby, Yvette M. Bordelon, Hugo Botha, Brad C Dickerson, Dennis W. Dickson, Kimiko Domoto-Reilly, Anne M. Fagan, Julie A. Fields, Jamie C Fong, Tatiana M. Foroud, Douglas R. Galasko, Ralitza H. Gavrilova, Daniel H. Geschwind, Jill S Goldman, Nupur Ghoshal, Neill R Graff-Radford, Jonathan Graff-Radford, Ian Grant, Murray Grossman, Ging-Yuek Robin Hsiung, Eric J. Huang, Edward D. Huey, David J Irwin, David T. Jones, David S. Knopman, John Kornak, Kejal Kantarci, Walter K. Kremers, Maria I. Lapid, Gabriel C Leger, Irene Litvan, Diane E. Lucente, Ian R MacKenzie, Joseph C. Masdeu, Corey T McMillan, Mario F. Mendez, Toji Miyagawa, Chiadi U. Onyike, Belen Pascual, Otto Pedraza, Leonard Petrucelli, Rosa Rademakers, Katherine P. Rankin, Katya Rascovsky, Jessica E Rexach, Aaron Ritter, Erik D Roberson, Maria Carmela Tartaglia, Arthur W. Toga, Sandra Weintraub, Bonnie Wong, Zbigniew Wszolek, Jeffrey L. Dage, Brad F. Boeve, Howard J. Rosen, Adam L. Boxer

Diagnostic Performance of Plasma P-tau217, NfL, and GFAP for Predicting Alzheimer’s Disease Neuropathology Across Diverse Neurodegenerative Syndromes.

Hanna Cho, Mark E. Sanderson-Cimino, Jonathan Tablante, Fattin Wekselman, Lea T. Grinberg, Hilary W. Heuer, Argentina Lario Lago, Peter A. Ljubenkov, Julio C. Rojas, William W. Seeley, Salvatore Spina, Adam M. Staffaroni, Gallen Triana-Baltzer, Hartmuth C. Kolb, Renaud La Joie, Gil D. Rabinovici, Adam L. Boxer, Lawren VandeVrede

CSF Proteomics in Patients With Progressive Supranuclear Palsy.

Wise A, Li J, Yamakawa M, Loureiro J, Peterson B, Worringer K, Sivasankaran R, Palma JA, Mitic L, Heuer HW, Lario-Lago A, Staffaroni AM, Clark A, Taylor J, Ljubenkov PA, Vandevrede L, Grinberg LT, Spina S, Seeley WW, Miller BL, Boeve BF, Dickerson BC, Grossman M, Litvan I, Pantelyat A, Tartaglia MC, Zhang Z, Wills AA, Rexach J, Rojas JC, Boxer AL, as the 4-Repeat Tauopathy Neuroimaging Initiative

Evaluating the Effect of Alzheimer's Disease-Related Biomarker Change in Corticobasal Syndrome and Progressive Supranuclear Palsy.

Garcia-Cordero I, Anastassiadis C, Khoja A, Morales-Rivero A, Thapa S, Vasilevskaya A, Davenport C, Sumra V, Couto B, Multani N, Taghdiri F, Anor C, Misquitta K, Vandevrede L, Heuer H, Tang-Wai D, Dickerson B, Pantelyat A, Litvan I, Boeve B, Rojas JC, Ljubenkov P, Huey E, Fox S, Kovacs GG, Boxer A, Lang A, Tartaglia MC, 4-R-Tauopathy Neuroimaging Initiative Consortium, and the Alzheimer's Disease Neuroimaging Initiativ

Large-scale network analysis of the cerebrospinal fluid proteome identifies molecular signatures of frontotemporal lobar degeneration.

Saloner R, Staffaroni A, Dammer E, Johnson ECB, Paolillo E, Wise A, Heuer H, Forsberg L, Lago AL, Webb J, Vogel J, Santillo A, Hansson O, Kramer J, Miller B, Li J, Loureiro J, Sivasankaran R, Worringer K, Seyfried N, Yokoyama J, Seeley W, Spina S, Grinberg L, VandeVrede L, Ljubenkov P, Bayram E, Bozoki A, Brushaber D, Considine C, Day G, Dickerson B, Domoto-Reilly K, Faber K, Galasko D, Geschwind D, Ghoshal N, Graff-Radford N, Hales C, Honig L, Hsiung GY, Huey E, Kornak J, Kremers W, Lapid M, Lee S, Litvan I, McMillan C, Mendez M, Miyagawa T, Pantelyat A, Pascual B, Paulson H, Petrucelli L, Pressman P, Ramos E, Rascovsky K, Roberson E, Savica R, Snyder A, Sullivan AC, Tartaglia C, Vandebergh M, Boeve B, Rosen H, Rojas J, Boxer A, Casaletto K

[18F]PI-2620 Binding Patterns in Patients with Suspected Alzheimer Disease and Frontotemporal Lobar Degeneration.

Blazhenets G, Soleimani-Meigooni DN, Thomas W, Mundada N, Brendel M, Vento S, VandeVrede L, Heuer HW, Ljubenkov P, Rojas JC, Chen MK, Amuiri AN, Miller Z, Gorno-Tempini ML, Miller BL, Rosen HJ, Litvan I, Grossman M, Boeve B, Pantelyat A, Tartaglia MC, Irwin DJ, Dickerson BC, Baker SL, Boxer AL, Rabinovici GD, La Joie R

Plasma inflammation for predicting phenotypic conversion and clinical progression of autosomal dominant frontotemporal lobar degeneration.

Asken BM, Ljubenkov PA, Staffaroni AM, Casaletto KB, Vandevrede L, Cobigo Y, Rojas-Rodriguez JC, Rankin KP, Kornak J, Heuer H, Shigenaga J, Appleby BS, Bozoki AC, Domoto-Reilly K, Ghoshal N, Huey E, Litvan I, Masdeu JC, Mendez MF, Pascual B, Pressman P, Tartaglia MC, Kremers W, Forsberg LK, Boeve BF, Boxer AL, Rosen HJ, Kramer JH, ALLFTD Consortium Investigators

The Neurofilament Surveillance Project (NSP): A biomarker study to sample blood quarterly in familial frontotemporal lobar degeneration.

Rachel Acuna-Narvaez, Hilary W. Heuer, Leah K. Forsberg, Anne Alward, Danielle Graham, Ann Fishman, Kevin M Nelson, Tyler Kolander, Howard M Fillit, Wendy R Galpern, Serena Hung, Chris Mason, Laurence Mignon, Yan G Ni, Arthur Simen, Ina Tesseur, Richard Tsai, Felix L Yeh, Carly T. Mester, Peter A. Ljubenkov, Howard J. Rosen, Bradley F. Boeve, Adam L. Boxer, Rodney Pearlman, Laura L Mitic, NSP Site Investigators

[18F]PI-2620 PET in four-repeat tauopathies: a preliminary study.

David N. Soleimani-Meigooni, Wesley P. Thomas, Matthias Brendel, Stephanie Vento, Hilary W. Heuer, Peter A. Ljubenkov, Julio C. Rojas, Miranda Chen, Leonardo Iaccarino, Renaud La Joie, Nidhi S. Mundada, Bradley F. Boeve, Murray Grossman, Bradford C. Dickerson, David J. Irwin, Irene Litvan, Alex Pantelyat, Carmela Tartaglia, Gil D. Rabinovici, Suzanne L. Baker, Adam L. Boxer

Temporal order of clinical and biomarker changes in familial frontotemporal dementia.

Staffaroni AM, Quintana M, Wendelberger B, Heuer HW, Russell LL, Cobigo Y, Wolf A, Goh SM, Petrucelli L, Gendron TF, Heller C, Clark AL, Taylor JC, Wise A, Ong E, Forsberg L, Brushaber D, Rojas JC, VandeVrede L, Ljubenkov P, Kramer J, Casaletto KB, Appleby B, Bordelon Y, Botha H, Dickerson BC, Domoto-Reilly K, Fields JA, Foroud T, Gavrilova R, Geschwind D, Ghoshal N, Goldman J, Graff-Radford J, Graff-Radford N, Grossman M, Hall MGH, Hsiung GY, Huey ED, Irwin D, Jones DT, Kantarci K, Kaufer D, Knopman D, Kremers W, Lago AL, Lapid MI, Litvan I, Lucente D, Mackenzie IR, Mendez MF, Mester C, Miller BL, Onyike CU, Rademakers R, Ramanan VK, Ramos EM, Rao M, Rascovsky K, Rankin KP, Roberson ED, Savica R, Tartaglia MC, Weintraub S, Wong B, Cash DM, Bouzigues A, Swift IJ, Peakman G, Bocchetta M, Todd EG, Convery RS, Rowe JB, Borroni B, Galimberti D, Tiraboschi P, Masellis M, Finger E, van Swieten JC, Seelaar H, Jiskoot LC, Sorbi S, Butler CR, Graff C, Gerhard A, Langheinrich T, Laforce R, Sanchez-Valle R, de Mendonça A, Moreno F, Synofzik M, Vandenberghe R, Ducharme S, Le Ber I, Levin J, Danek A, Otto M, Pasquier F, Santana I, Kornak J, Boeve BF, Rosen HJ, Rohrer JD, Boxer AL, Frontotemporal Dementia Prevention Initiative (FPI) Investigators

Clinical value of CSF tau, p-tau181, neurogranin and neurofilaments in familial frontotemporal lobar degeneration.

Julio C. Rojas, Hilary W. Heuer, Weiping Chen, Julie Czerkowicz, Danielle Graham, Leah K. Forsberg, Danielle Brushaber, Brian Appleby, Eliana Marisa Ramos, Giovanni Coppolla, Yvette M. Bordelon, Hugo Botha, Brad C. Dickerson, Dennis W. Dickson, Kimiko Domoto-Reilly, Anne M. Fagan, Julie A. Fields, Jamie C. Fong, Tatiana M. Foroud, Doug R. Galasko, Ralitza H. Gavrilova, Daniel H. Geschwind, Nupur Ghoshal, Jill Goldman, Neill R. Graff-Radford, Jonathan Graff-Radford, Ian Grant, Murray Grossman, Ging-Yuek Robin Hsiung, Eric J. Huang, Edward D. Huey, David J. Irwin, David T. Jones, Kejal Kantarci, David S. Knopman, John Kornak, Walter K. Kremers, Maria I. Lapid, Gabriel C. Leger, Irene Litvan, Peter A. Ljubenkov, Diane E. Lucente, Ian R Mackenzie, Joseph C. Masdeu, Corey T. McMillan, Mario F. Mendez, Bruce L. Miller, Toji Miyagawa, Chiadi U. Onyike, Belen Pascual, Otto Pedraza, Leonard Petrucelli, Rosa Rademakers, Katherine P. Rankin, Katya Rascovsky, Jessica E. Rexach, Aaron Ritter, Erik D. Roberson, Rodolfo Savica, William W. Seeley, Adam M. Staffaroni, Maria Carmela Tartaglia, Arthur W. Toga, Sandra Weintraub, Bonnie Wong, Zbigniew Wszolek, Lawren Vandevrede, Bradley F. Boeve, Howard J. Rosen, Adam L. Boxer

Demographic and psychosocial factors associated with the decision to learn mutation status in familial frontotemporal dementia and the impact of disclosure on mood.

Lynn P. Bajorek, Rachel Kiekhofer, Matthew Hall, Joanne Taylor, Diane E Lucente, Danielle Brushaber, Brian Appleby, Giovanni Coppolla, Yvette M Bordelon, Hugo Botha, Brad C Dickerson, Dennis W Dickson, Kimiko Domoto-Reilly, Anne M Fagan, Julie A Fields, Jamie C Fong, Tatiana M Foroud, Leah K Forsberg, Doug R Galasko, Ralitza H Gavrilova, Daniel H Geschwind, Nupur Ghoshal, Jill Goldman, Neill R Graff-Radford, Jonathan Graff-Radford, Ian Grant, Murray Grossman, Hilary W Heuer, Ging-Yuek Robin Hsiung, Eric J Huang, Edward D Huey, David J Irwin, David T Jones, Kejal Kantarci, John Kornak, Walter K Kremers, Maria I Lapid, Gabriel C Leger, Irene Litvan, Peter A Ljubenkov, Ian R Mackenzie, Joseph C Masdeu, Corey McMillan, Mario Mendez, Bruce L Miller, Toji Miyagawa, Chiadi U Onyike, Belen Pascual, Otto Pedraza, Leonard Petrucelli, Rosa Rademakers, Eliana Marisa Ramos, Katherine P Rankin, Katya Rascovsky, Jessica E Rexach, Aaron Ritter, Erik D. Roberson, Rodolfo Savica, Julio C Rojas, William W Seeley, Maria Carmela Tartaglia, Arthur W Toga, Sandra Weintraub, Bonnie Wong, Zbigniew Wszolek, Lawren Vandevrede, Bradley F Boeve, Adam L Boxer, Howard J Rosen, Adam M Staffaroni, ALLFTD Consortium

Diagnostic value of plasma P-tau217 in frontotemporal dementia spectrum disorders.

Julio C. Rojas, Lawren Vandevrede, Hilary W. Heuer, Gianina Toller, Elisabeth H. Thijssen, Nicholas Proctor, Leah K. Forsberg, Danielle Brushaber, Eliana Marisa Ramos, Giovanni Coppola, Brian Appleby, Yvette M. Bordelon, Hugo Botha, Brad C. Dickerson, Dennis W. Dickson, Kimiko Domoto-Reilly, Anne M. Fagan, Julie A. Fields, Jamie C. Fong, Tatiana M. Foroud, Doug R. Galasko, Ralitza H. Gavrilova, Daniel H. Geschwind, Nupur Ghoshal, Jill Goldman, Neill R. Graff-Radford, Jonathan Graff-Radford, Ian Grant, Murray Grossman, Ging-Yuek Robin Hsiung, Eric J. Huang, Edward D. Huey, David J. Irwin, David T. Jones, Kejal Kantarci, David S. Knopman, John Kornak, Walter K. Kremers, Maria I. Lapid, Gabriel C. Leger, Irene Litvan, Peter A. Ljubenkov, Diane E. Lucente, Ian R. Mackenzie, Joseph C. Masdeu, Corey T. McMillan, Mario Mendez, Bruce L. Miller, Toji Miyagawa, Chiadi U. Onyike, Belen Pascual, Otto Pedraza, Leonard Petrucelli, Rosa Rademakers, Katherine P. Rankin, Katya Rascovsky, Jessica E. Rexach, Aaron Ritter, Erik D. Roberson, Rodolfo Savica, William W. Seeley, Adam M. Staffaroni, Maria Carmela Trataglia, Arthur W. Toga, Sandra Weintraub, Bonnie Wong, Zbigniew Wszolek, Jeffrey L. Dage, Bradley F. Boeve, Howard J. Rosen, Adam L. Boxer

Gearing up for the future: Exploring facilitators and barriers to inform clinical trial design in frontotemporal lobar degeneration.

Yasmin B Banga, Yujung Lai, Priscilla Kim, Bradley F Boeve, Adam L Boxer, Howard J Rosen, Leah K Forsberg, Hilary W Heuer, Danielle Brushaber, Brian Appleby, Joanna M Biernacka, Yvette M Bordelon, Hugo Botha, Andrea C Bozoki, Patrick Brannelly, Brad C Dickerson, Susan Dickinson, Dennis W Dickson, Kimiko Domoto-Reilly, Kelley Faber, Anne M Fagan, Julie A Fields, Ann Fishman, Tatiana M Foroud, Doug R Galasko, Ralitza H Gavrilova, Tania F Gendron, Daniel H Geschwind, Nupur Ghoshal, Jill Goldman, Jonathan Graff-Radford, Neill R Graff-Radford, Ian Grant, Murray Grossman, Ging-Yuek Robin Hsiung, Eric J Huang, Edward D Huey, David J Irwin, David T Jones, Kejal Kantarci, Anna M Karydas, Daniel Kaufer, David S Knopman, Joel H Kramer, Walter K Kremers, John Kornak, Walter A Kukull, Emma Lagone, Gabriel C Leger, Irene Litvan, Peter A Ljubenkov, Diane E Lucente, Ian R Mackenzie, Masood Manoochehri, Joseph C Masdeu, Scott McGinnis, Mario F Mendez, Bruce L Miller, Toji Miyagawa, Kevin M Nelson, Chiadi U Onyike, Alex Pantelyat, Belen Pascual, Rodney Pearlman, Leonard Petrucelli, Cyril P Pottier, Rosa Rademakers, Eliana Marisa Ramos, Katherine P Rankin, Katya Rascovsky, Jessica E Rexach, Aaron Ritter, Erik D Roberson, Julio C Rojas, Marwan N Sabbagh, David P Salmon, Rodolfo Savica, William W Seeley, Adam M Staffaroni, Jeremy A Syrjanen, Maria Carmela Tartaglia, Nadine Tatton, Jack C Taylor, Arthur W Toga, Sandra Weintraub, Diana Wheaton, Benjamin Wong, Zbigniew Wszolek, ALLFTD Consortium

Effect of the Histone Deacetylase Inhibitor FRM-0334 on Progranulin Levels in Patients With Progranulin Gene Haploinsufficiency: A Randomized Clinical Trial.

Ljubenkov PA, Edwards L, Iaccarino L, La Joie R, Rojas JC, Koestler M, Harris B, Boeve BF, Borroni B, van Swieten JC, Grossman M, Pasquier F, Frisoni GB, Mummery CJ, Vandenberghe R, Le Ber I, Hannequin D, McGinnis SM, Auriacombe S, Onofrj M, Goodman IJ, Riordan HJ, Wisniewski G, Hesterman J, Marek K, Haynes BA, Patzke H, Koenig G, Hilt D, Moebius H, Boxer AL

Best Practices in the Clinical Management of Progressive Supranuclear Palsy and Corticobasal Syndrome: A Consensus Statement of the CurePSP Centers of Care.

Bluett B, Pantelyat AY, Litvan I, Ali F, Apetauerova D, Bega D, Bloom L, Bower J, Boxer AL, Dale ML, Dhall R, Duquette A, Fernandez HH, Fleisher JE, Grossman M, Howell M, Kerwin DR, Leegwater-Kim J, Lepage C, Ljubenkov PA, Mancini M, McFarland NR, Moretti P, Myrick E, Patel P, Plummer LS, Rodriguez-Porcel F, Rojas J, Sidiropoulos C, Sklerov M, Sokol LL, Tuite PJ, VandeVrede L, Wilhelm J, Wills AA, Xie T, Golbe LI

Plasma Neurofilament Light for Prediction of Disease Progression in Familial Frontotemporal Lobar Degeneration.

Rojas JC, Wang P, Staffaroni AM, Heller C, Cobigo Y, Wolf A, Goh SM, Ljubenkov PA, Heuer HW, Fong JC, Taylor JB, Veras E, Song L, Jeromin A, Hanlon D, Yu L, Khinikar A, Sivasankaran R, Kieloch A, Valentin MA, Karydas AM, Mitic LL, Pearlman R, Kornak J, Kramer JH, Miller BL, Kantarci K, Knopman DS, Graff-Radford N, Petrucelli L, Rademakers R, Irwin DJ, Grossman M, Ramos EM, Coppola G, Mendez MF, Bordelon Y, Dickerson BC, Ghoshal N, Huey ED, Mackenzie IR, Appleby BS, Domoto-Reilly K, Hsiung GR, Toga AW, Weintraub S, Kaufer DI, Kerwin D, Litvan I, Onyike CU, Pantelyat A, Roberson ED, Tartaglia MC, Foroud T, Chen W, Czerkowicz J, Graham DL, van Swieten JC, Borroni B, Sanchez-Valle R, Moreno F, Laforce R, Graff C, Synofzik M, Galimberti D, Rowe JB, Masellis M, Finger E, Vandenberghe R, de Mendonça A, Tagliavini F, Santana I, Ducharme S, Butler CR, Gerhard A, Levin J, Danek A, Otto M, Sorbi S, Cash DM, Convery RS, Bocchetta M, Foiani M, Caroline V G, Peakman G, Russell L, Swift I, Todd E, Rohrer JD, Boeve BF, Rosen HJ, Boxer AL

Neuropsychiatric abnormalities in familial frontotemporal dementia: Findings from the LEFFTDS Cohort.

Leah K. Forsberg, Bradley F. Boeve, Howard J. Rosen, Adam L. Boxer, Jeremy Syrjanen, Danielle Brushaber, Giovanni Coppolla, Brad C. Dickerson, Julie A. Fields, Jamie Fong, Ralitza H. Gavrilova, Nupur Ghoshal, Jill Goldman, Jonathan Graff-Radford, Neill R. Graff-Radford, Murray Grossman, Hilary W. Heuer, Ging-Yuek Robin Hsiung, Edward Huey, David J. Irwin, David T. Jones, Kejal Kantarci, Anna M. Karydas, David S. Knopman, John Kornak, Joel H. Kramer, Walter K. Kremers, Walter A. Kukull, Peter A. Ljubenkov, Ian R. Mackenzie, Scott McGinnis, Bruce L. Miller, Rosa Rademakers, Eliana Marisa Ramos, Katherine Rankin, Katya Rascovsky, Virginia Sturm, Adam M. Staffaroni, Joanne Taylor, Bonnie Wong, Zbigniew Wszolek

Plasma neurofilament light chain levels reflect caregiver burden and social cognition measures in familial frontotemporal lobar degeneration (FTLD).

Hilary W. Heuer, Julio C. Rojas, Gianina Toller, Katherine Rankin, Danielle Brushaber, Brian Appleby, Yvette M. Bordelon, Brad C. Dickerson, Domoto-Reilly Kimiko, Kelley Faber, Tatiana M. Foroud, Leah K Forsberg, Nupur Ghoshal, Ian Grant, Neill R. Graff-Radford, Murray Grossman, Ging-Yuek Robin Hsiung, Edward D. Huey, Anna M. Karydas, Daniel Kaufer, Diana R. Kerwin, Emma Lagone, Irene Litvan, Peter A. Ljubenkov, Ian R. Mackenzie, Mario F. Mendez, Bruce L. Miller, Chiadi U. Onyike, Eliana Marisa Ramos, Katya Rascovsky, Erik D. Roberson, Carmela Tartaglia, Sandra Weintraub, Bradley F. Boeve, Howard J. Rosen, Adam L. Boxer, ARTFL/LEFFTDS Investigators

Studying the natural history of frontotemporal lobar degeneration (FTLD): The ARTFL LEFFTDS longitudinal FTLD (ALLFTD) protocol.

Bradley F. Boeve, Adam L. Boxer, Howard J. Rosen, Leah K. Forsberg, Hilary W. Heuer, Danielle Brushaber, Brian Appleby, Joanna M. Biernacka, Yvette M. Bordelon, Hugo Botha, Patrick Brannelly, Brad C. Dickerson, Dennis W. Dickson, Domoto-Reilly Kimiko, Kelley Faber, Anne Fagan, Julie A. Fields, Ann Fishman, Tatiana M. Foroud, Doug R. Galasko, Ralitza H. Gavrilova, Tania F. Gendron, Daniel H. Geschwind, Nupur Ghoshal, Jill Goldman, Jonathan Graff-Radford, Neill R. Graff-Radford, Ian Grant, Murray Grossman, Ging-Yuek Robin Hsiung, Eric J. Huang, Edward Huey, David J. Irwin, David T. Jones, Kejal Kantarci, Anna M. Karydas, Daniel Kaufer, David S. Knopman, Joel H. Kramer, Walter K. Kremers, John Kornak, Walter A. Kukull, Emma Lagone, Gabriel C. Leger, Irene Litvan, Peter A. Ljubenkov, Diane E Lucente, Ian R Mackenzie, Masood Manoochehri, Joseph C. Masdeu, Scott McGinnis, Mario F. Mendez, Bruce L. Miller, Toji Miyagawa, Kevin M. Nelson, Chiadi U Onyike, Alex Pantelyat, Belen Pascual, Rodney Pearlman, Leonard Petrucelli, Rosa Rademakers, Eliana Marisa Ramos, Katherine Rankin, Katya Rascovsky, Jessica E. Rexach, Aaron Ritter, Erik D. Roberson, Julio C. Rojas, Marwan N. Sabbagh, David P. Salmon, Rodolfo Savica, William W. Seeley, Adam M. Staffaroni, Jeremy Syrjanen, Carmela Tartaglia, Nadine Tatton, Joanne Taylor, Arthur W. Toga, Sandra Weintraub, Diana Wheaton, Bonnie Wong, Zbigniew Wszolek

The ARTFL LEFFTDS Frontotemporal Lobar Degeneration (ALLFTD) Protocol: Preliminary Data and Future Plans (2081).

Bradley Boeve, Adam Boxer, Howard Rosen, Leah Forsberg, Hilary Heuer, Danielle Brushaber, Brian Appleby, Joanna Biernacka, Yvette Bordelon, Hugo Botha, Patrick Brannelly, Bradford Dickerson, Susan Dickinson, Dennis Dickson, Kimiko Domoto-Reilly, Kelley Faber, Anne Fagan, Julie Fields, Ann Fishman, Tatiana Foroud, Douglas Galasko, Ralitza Gavrilova, Tania Gendron, Daniel Geschwind, Nupur Ghoshal, Jill Goldman, Jonathan Graff-Radford, Neill Graff-Radford, Ian Grant, Murray Grossman, Ging-Yuek Hsiung, Eric Huang, Edward Huey, David Irwin, David Jones, Kejal Kantarci, Anna Karydas, Daniel Kaufer, David Knopman, Joel Kramer, Walter Kremers, John Kornak, Walter Kukull, Emma Lagone, Irene Litvan, Peter Ljubenkov, Diane Lucente, Ian R.A. Mackenzie, Masood Manoochehri, Joseph Masdeu, Scott McGinnis, Mario Mendez, Bruce Miller, Toji Miyagawa, Kevin Nelson, Chiadi Onyike, Alexander Pantelyat, Belen Pascual, Rodney Pearlman, Leonard Petrucelli, Rosa Rademakers, Eliana Marisa Ramos, Katherine Rankin, Katya Rascovsky, Jessica Rexach, Aaron Ritter, Erik Roberson, Julio Rojas -Martinez, Marwan Sabbagh, David Salmon, Rodolfo Savica, William Seeley, Adam Staffaroni, Jeremy Syrjanen, Carmela Tartaglia, Nadine Tatton, Joanne Taylor, Arthur Toga, Sandra Weintraub, Diana Wheaton, Bonnie Wong, Zbigniew Wszolek

Clinical and volumetric changes with increasing functional impairment in familial frontotemporal lobar degeneration.

Olney NT, Ong E, Goh SM, Bajorek L, Dever R, Staffaroni AM, Cobigo Y, Bock M, Chiang K, Ljubenkov P, Kornak J, Heuer HW, Wang P, Rascovsky K, Wolf A, Appleby B, Bove J, Bordelon Y, Brannelly P, Brushaber D, Caso C, Coppola G, Dickerson BC, Dickinson S, Domoto-Reilly K, Faber K, Ferrall J, Fields J, Fishman A, Fong J, Foroud T, Forsberg LK, Gearhart DJ, Ghazanfari B, Ghoshal N, Goldman J, Graff-Radford J, Graff-Radford NR, Grant I, Grossman M, Haley D, Hsiung G, Huey ED, Irwin DJ, Jones DT, Kantarci K, Karydas AM, Kaufer D, Kerwin D, Knopman DS, Kramer JH, Kraft R, Kremers W, Kukull W, Lapid MI, Litvan I, Mackenzie IR, Maldonado M, Manoochehri M, McGinnis SM, McKinley EC, Mendez MF, Miller BL, Onyike C, Pantelyat A, Pearlman R, Petrucelli L, Potter M, Rademakers R, Ramos EM, Rankin KP, Roberson ED, Rogalski E, Sengdy P, Shaw LM, Syrjanen J, Tartaglia MC, Tatton N, Taylor J, Toga A, Trojanowski JQ, Weintraub S, Wong B, Wszolek Z, Boxer AL, Boeve BF, Rosen HJ

Individualized atrophy scores predict dementia onset in familial frontotemporal lobar degeneration.

Staffaroni AM, Cobigo Y, Goh SM, Kornak J, Bajorek L, Chiang K, Appleby B, Bove J, Bordelon Y, Brannelly P, Brushaber D, Caso C, Coppola G, Dever R, Dheel C, Dickerson BC, Dickinson S, Dominguez S, Domoto-Reilly K, Faber K, Ferrall J, Fields JA, Fishman A, Fong J, Foroud T, Forsberg LK, Gavrilova R, Gearhart D, Ghazanfari B, Ghoshal N, Goldman J, Graff-Radford J, Graff-Radford N, Grant I, Grossman M, Haley D, Heuer HW, Hsiung GY, Huey ED, Irwin DJ, Jones DT, Jones L, Kantarci K, Karydas A, Kaufer DI, Kerwin DR, Knopman DS, Kraft R, Kramer JH, Kremers WK, Kukull WA, Litvan I, Ljubenkov PA, Lucente D, Lungu C, Mackenzie IR, Maldonado M, Manoochehri M, McGinnis SM, McKinley E, Mendez MF, Miller BL, Multani N, Onyike C, Padmanabhan J, Pantelyat A, Pearlman R, Petrucelli L, Potter M, Rademakers R, Ramos EM, Rankin KP, Rascovsky K, Roberson ED, Rogalski E, Sengdy P, Shaw LM, Syrjanen J, Tartaglia MC, Tatton N, Taylor J, Toga A, Trojanowski JQ, Weintraub S, Wang P, Wong B, Wszolek Z, Boxer AL, Boeve BF, Rosen HJ

Assessment of executive function declines in presymptomatic and mildly symptomatic familial frontotemporal dementia: NIH-EXAMINER as a potential clinical trial endpoint.

Staffaroni AM, Bajorek L, Casaletto KB, Cobigo Y, Goh SM, Wolf A, Heuer HW, Elahi FM, Ljubenkov PA, Dever R, Kornak J, Appleby B, Bove J, Bordelon Y, Brannelly P, Brushaber D, Caso C, Coppola G, Dheel C, Dickerson BC, Dickinson S, Dominguez S, Domoto-Reilly K, Faber K, Ferrall J, Fields JA, Fishman A, Fong J, Foroud T, Forsberg LK, Gavrilova R, Gearhart D, Ghazanfari B, Ghoshal N, Goldman J, Graff-Radford J, Graff-Radford N, Grant I, Grossman M, Haley D, Hsiung GY, Huey ED, Irwin DJ, Jones DT, Jones L, Kantarci K, Karydas A, Kaufer DI, Kerwin DR, Knopman DS, Kraft R, Kremers WK, Kukull WA, Litvan I, Lucente D, Lungu C, Mackenzie IR, Maldonado M, Manoochehri M, McGinnis SM, McKinley E, Mendez MF, Miller BL, Multani N, Onyike C, Padmanabhan J, Pantelyat A, Pearlman R, Petrucelli L, Potter M, Rademakers R, Ramos EM, Rankin KP, Rascovsky K, Roberson ED, Rogalski E, Sengdy P, Shaw LM, Syrjanen J, Tartaglia MC, Tatton N, Taylor J, Toga A, Trojanowski JQ, Weintraub S, Wang P, Wong B, Wszolek Z, Boxer AL, Boeve BF, Kramer JH, Rosen HJ

Comparison of sporadic and familial behavioral variant frontotemporal dementia (FTD) in a North American cohort.

Heuer HW, Wang P, Rascovsky K, Wolf A, Appleby B, Bove J, Bordelon Y, Brannelly P, Brushaber DE, Caso C, Coppola G, Dickerson B, Dickinson S, Domoto-Reilly K, Faber K, Ferrall J, Fields J, Fishman A, Fong J, Foroud T, Forsberg LK, Gearhart D, Ghazanfari B, Ghoshal N, Goldman J, Graff-Radford J, Graff-Radford N, Grant I, Grossman M, Haley D, Hsiung GY, Huey E, Irwin D, Jones D, Kantarci K, Karydas A, Kaufer D, Kerwin D, Knopman D, Kornak J, Kramer JH, Kraft R, Kremers WK, Kukull W, Litvan I, Ljubenkov P, Mackenzie IR, Maldonado M, Manoochehri M, McGinnis S, McKinley E, Mendez MF, Miller BL, Onyike C, Pantelyat A, Pearlman R, Petrucelli L, Potter M, Rademakers R, Ramos EM, Rankin KP, Roberson ED, Rogalski E, Sengdy P, Shaw L, Syrjanen J, Tartaglia MC, Tatton N, Taylor J, Toga A, Trojanowski J, Weintraub S, Wong B, Wszolek Z, Boeve BF, Rosen HJ, Boxer AL

Genetic screening of a large series of North American sporadic and familial frontotemporal dementia cases.

Ramos EM, Dokuru DR, Van Berlo V, Wojta K, Wang Q, Huang AY, Deverasetty S, Qin Y, van Blitterswijk M, Jackson J, Appleby B, Bordelon Y, Brannelly P, Brushaber DE, Dickerson B, Dickinson S, Domoto-Reilly K, Faber K, Fields J, Fong J, Foroud T, Forsberg LK, Gavrilova R, Ghoshal N, Goldman J, Graff-Radford J, Graff-Radford N, Grant I, Grossman M, Heuer HW, Hsiung GR, Huey E, Irwin D, Kantarci K, Karydas A, Kaufer D, Kerwin D, Knopman D, Kornak J, Kramer JH, Kremers W, Kukull W, Litvan I, Ljubenkov P, Lungu C, Mackenzie I, Mendez MF, Miller BL, Onyike C, Pantelyat A, Pearlman R, Petrucelli L, Potter M, Rankin KP, Rascovsky K, Roberson ED, Rogalski E, Shaw L, Syrjanen J, Tartaglia MC, Tatton N, Taylor J, Toga A, Trojanowski JQ, Weintraub S, Wong B, Wszolek Z, Rademakers R, Boeve BF, Rosen HJ, Boxer AL, Coppola G

Nonlinear Z-score modeling for improved detection of cognitive abnormality.

Kornak J, Fields J, Kremers W, Farmer S, Heuer HW, Forsberg L, Brushaber D, Rindels A, Dodge H, Weintraub S, Besser L, Appleby B, Bordelon Y, Bove J, Brannelly P, Caso C, Coppola G, Dever R, Dheel C, Dickerson B, Dickinson S, Dominguez S, Domoto-Reilly K, Faber K, Ferrall J, Fishman A, Fong J, Foroud T, Gavrilova R, Gearhart D, Ghazanfari B, Ghoshal N, Goldman J, Graff-Radford J, Graff-Radford N, Grant IM, Grossman M, Haley D, Hsiao J, Hsiung R, Huey ED, Irwin D, Jones D, Jones L, Kantarci K, Karydas A, Kaufer D, Kerwin D, Knopman D, Kraft R, Kramer J, Kukull W, Lapid M, Litvan I, Ljubenkov P, Lucente D, Lungu C, Mackenzie I, Maldonado M, Manoochehri M, McGinnis S, McKinley E, Mendez M, Miller B, Multani N, Onyike C, Padmanabhan J, Pantelyat A, Pearlman R, Petrucelli L, Potter M, Rademakers R, Ramos EM, Rankin K, Rascovsky K, Roberson ED, Rogalski-Miller E, Sengdy P, Shaw L, Staffaroni AM, Sutherland M, Syrjanen J, Tartaglia C, Tatton N, Taylor J, Toga A, Trojanowski J, Wang P, Wong B, Wszolek Z, Boeve B, Boxer A, Rosen H

FRONTOTEMPORAL LOBAR DEGENERATION RESEARCH IN NORTH AMERICA: PROGRESS IN THE ARTFL/LEFFTDS CONSORTIA.

Hilary W. Heuer, Adam L. Boxer, Bradley F. Boeve, Howard J. Rosen, Leah K. Forsberg, Danielle Brushaber, Brian Appleby, Yvette M. Bordelon, Patrick Brannelly, Giovanni Coppola, Brad C. Dickerson, Susan Dickinson, Domoto-Reilly Kimiko, Kelley Faber, Julie A. Fields, Jamie Fong, Tatiana M. Foroud, Ralitza H. Gavrilova, Nupur Ghoshal, Jill Goldman, Jonathan Graff-Radford, Neil R. Graff-Radford, Ian Grant, Murray Grossman, John Hsiao, Ging-Yuek Robin Hsiung, Edward Huey, David Irwin, Kejal Kantarci, Anna M. Karydas, Daniel Kaufer, Diana R. Kerwin, David S. Knopman, Joel H. Kramer, Walter K. Kremers, Walter A. Kukull, Irene Litvan, Peter A. Ljubenkov, Diane E. Lucente, Codrin Lungu, Ian R. Mackenzie, Scott M. McGinnis, Mario F. Mendez, Bruce L. Miller, Chiadi U. Onyike, Alex Pantelyat, Rodney Pearlman, Leonard Petrucelli, Rosa Rademakers, Eliana Marisa Ramos, Katherine Rankin, Katya Rascovsky, Erik D. Roberson, Emily J. Rogalski, Leslie M. Shaw, Margaret Sutherland, Jeremy Syrjanen, Carmela Tartaglia, Nadine Tatton, Joanne Taylor, Arthur W. Toga, Sandra Weintraub, Bonnie Wong, Zbigniew Wszolek, ARTFL and LEFFTDS Consortia

THE MULTIDOMAIN IMPAIRMENT RATING (MIR) SCALE: INITIAL RELIABILITY DATA ON A MULTIDIMENSIONAL SCALE DESIGNED FOR FTLD SPECTRUM DISORDERS.

Leah K. Forsberg, Bradley F. Boeve, Adam L. Boxer, Howard J. Rosen, John Kornak, Hilary W. Heuer, Julie A. Fields, Danielle Brushaber, Mary M. Machulda, Virginia Sturm, Adam M. Staffaroni, Peter A. Ljubenkov, Reilly Denver, Elise Ong, Brian Appleby, Yvette M. Bordelon, Patrick Brannelly, Giovanni Coppola, Brad C. Dickerson, Susan Dickinson, Domoto-Reilly Kimiko, Kelley Faber, Jamie Fong, Tatiana M. Foroud, Ralitza H. Gavrilova, Debra Gearhart, Nupur Ghoshal, Jill Goldman, Jonathan Graff-Radford, Neil R. Graff-Radford, Murray Grossman, Ging-Yuek Robin Hsiung, Edward D. Huey, David Irwin, David T. Jones, Kejal Kantarci, Anna M. Karydas, Daniel Kaufer, Diana R. Kerwin, David S. Knopman, Ruth A. Kraft, Joel H. Kramer, Walter K. Kremers, Walter A. Kukull, Irene Litvan, Diane E. Lucente, Codrin Lungu, Ian R. Mackenzie, Scott M. McGinnis, Mario F. Mendez, Bruce L. Miller, Chiadi U. Onyike, Alex Pantelyat, Rodney Pearlman, Leonard Petrucelli, Madeline Potter, Rosa Rademakers, Eliana Marisa Ramos, Katherine Rankin, Katya Rascovsky, Erik D. Roberson, Emily J. Rogalski, Leslie M. Shaw, Marg Sutherland, Jeremy Syrjanen, Carmela Tartaglia, Nadine Tatton, Joanne Taylor, Arthur W. Toga, John Q. Trojanowski, Sandra Weintraub, Bonnie Wong, Zbigniew Wszolek

THE NIH-EXAMINER IS SENSITIVE TO COGNITIVE CHANGES IN ASYMPTOMATIC AND MILDLY SYMPTOMATIC FAMILIAL FRONTOTEMPORAL DEMENTIA.

Adam M. Staffaroni, Lynn Bajorek, Peter Ljubenkov, Kaitlin Casaletto, Fanny Elahi, Katya Rascovsky, Bradley F. Boeve, Adam L. Boxer, Jessica Bove, Danielle Brushaber, Giovanni Coppola, Christina Dheel, Brad C. Dickerson, Julie A. Fields, Jamie Fong, Leah K. Forsberg, Ralitza H. Gavrilova, Debra Gearhart, Nupur Ghoshal, Jill Goldman, Jonathan Graff Radford, Neill R. Graff-Radford, Murray Grossman, Dana Haley, Hilary W. Heuer, John Hsiao, Ging-Yuek Robin Hsiung, Edward Huey, David J. Irwin, David T. Jones, Lynne Jones, Kejal Kantarci, Anna M. Karydas, David S. Knopman, John Kornak, Walter K. Kremers, Walter A. Kukull, Maria I. Lapid, Diane Lucente, Ian R. Mackenzie, Masood Manoochehri, Bruce L. Miller, Madeline Potter, Rosa Rademakers, Katherine Rankin, Margaret Sutherland, Jeremy Syrjanen, Joanne Taylor, Sandra Weintraub, Bonnie Wong, Zbigniew Wszolek, Howard J. Rosen, Joel H. Kramer, ARTFL/LEFFTDS Consortium